Atypical TeratoidJRhabdoid Tumour of Brain

Primitive neuroectodermal tumor (PNET) / medulloblastoma (MB) are the most common malignant central nervous tumors of the first decade of life. Atypical teratoid / rhabdoid tumor (ATT / RT) is a tumor of infancy and childhood although occasional cases have also been described in adults. ATT/RT has a characteristic histopathological, immunocytochemical and ultrastructural features. ATT /RT is a rare tumor, incidence of which remains to be defined with only hundred published cases. The present report docurilents the clinical features, histological and immunohistochemical findings of a case of ATT / RT.